Abstract
#Klippel-Trenaunay-Weber syndrome is a rare congenital
disorder characterized by the triad of capillary malformations,
bony or soft tissue hypertrophy usually of lower limbs, and #venous varicosities or malformations [1], both genders are equally affected.
The prevalence is estimated 1 in 20 000 to 1 in 100 000 live births
[2]. A 25-year-old male with Klippel - Trenaunay - Weber syndrome (KTWS)
presented with a new onset atrial fibrillation in May 2013 without
reversion to #sinusrhythm. His medical history included varicose disease
in lower limbs (Figure 1), mental retardation and a history of
progressive #dyspnea. Initial assessment was done with an echo showing a
dilatation of left atrium (LA), generalized left ventricular #hypokinesia
(LVHY), ejection fraction (EF): 40% with preserved right ventricular
function, moderate mitral insufficiency, pulmonary and tricuspid mild
insufficiency without evidence of #pulmonaryhypertension (Figure 2).
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For more Research and Review Articles on BJSTR
Klippel-Trenaunay-Weber #Syndrome and Heart Failure, an Uncommon Presentation by Gian Manuel Jiménez-Rodríguez in BJSTR
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